{"id":136687,"date":"2026-09-08T12:23:08","date_gmt":"2026-09-08T03:23:08","guid":{"rendered":"https:\/\/www.hiro-clinic.or.jp\/nipt\/?post_type=genetic-diseases&#038;p=136687"},"modified":"2026-09-08T12:23:08","modified_gmt":"2026-09-08T03:23:08","slug":"factor-vii-deficiency-f7","status":"publish","type":"genetic-diseases","link":"https:\/\/www.hiro-clinic.or.jp\/nipt\/genetic-diseases2\/factor-vii-deficiency-f7\/","title":{"rendered":"\u7b2cVII\u56e0\u5b50\u6b20\u4e4f\u75c7"},"content":{"rendered":"\n<h2 class=\"wp-block-heading\">\u6982\u8981<\/h2>\n\n\n\n<p>\u7b2cVII\u56e0\u5b50\u6b20\u4e4f\u75c7\u306f\u3001\u8840\u3092\u6b62\u3081\u308b\u305f\u3081\u306b\u5fc5\u8981\u306a\u305f\u3093\u3071\u304f\u8cea\uff08\u51dd\u56fa\u7b2cVII\u56e0\u5b50\uff09\u304c\u4e0d\u8db3\u3059\u308b\u305f\u3081\u306b\u3001\u51fa\u8840\u3057\u3084\u3059\u304f\u306a\u308b\u75c5\u6c17\u3067\u3059\u3002\u5e38\u67d3\u8272\u4f53\u6f5c\u6027\uff08\u52a3\u6027\uff09\u907a\u4f1d\u306e\u5f62\u5f0f\u3092\u3068\u308a\u3001<strong>F7<\/strong> \u907a\u4f1d\u5b50\u306e\u5909\u5316\u304c\u539f\u56e0\u3068\u306a\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<p><strong>\u307e\u308c\u306a\u51dd\u56fa\u56e0\u5b50\u6b20\u4e4f\u75c7\u306e\u306a\u304b\u3067\u306f\u3082\u3063\u3068\u3082\u983b\u5ea6\u304c\u9ad8\u3044<\/strong>\u75c5\u6c17\u3067\u3059\u3002\u75c7\u72b6\u306e\u91cd\u3055\u306b\u306f\u5927\u304d\u306a\u5e45\u304c\u3042\u308a\u3001\u5065\u5eb7\u8a3a\u65ad\u306e\u8840\u6db2\u691c\u67fb\u3067\u5076\u7136\u898b\u3064\u304b\u3063\u3066\u7121\u75c7\u72b6\u306e\u65b9\u304b\u3089\u3001\u4e73\u5150\u671f\u306b\u982d\u84cb\u5185\u51fa\u8840\u3092\u8d77\u3053\u3059\u65b9\u307e\u3067\u3055\u307e\u3056\u307e\u3067\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u539f\u56e0<\/h2>\n\n\n\n<p><strong>F7<\/strong> \u907a\u4f1d\u5b50\u306f\u3001\u809d\u81d3\u3067\u4f5c\u3089\u308c\u308b\u51dd\u56fa\u7b2cVII\u56e0\u5b50\u306e\u8a2d\u8a08\u56f3\u3067\u3059\u3002\u7b2cVII\u56e0\u5b50\u306f\u3001\u8840\u7ba1\u304c\u50b7\u3064\u3044\u305f\u3068\u304d\u306b\u7d44\u7e54\u56e0\u5b50\u3068\u7d50\u3073\u3064\u3044\u3066\u3001\u8840\u6db2\u3092\u56fa\u3081\u308b\u53cd\u5fdc\uff08\u5916\u56e0\u7cfb\uff09\u306e<strong>\u3044\u3061\u3070\u3093\u6700\u521d\u306e\u30b9\u30a4\u30c3\u30c1<\/strong>\u3092\u5165\u308c\u308b\u5f79\u76ee\u3092\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u3053\u306e\u56e0\u5b50\u304c\u4e0d\u8db3\u3059\u308b\u3068\u3001\u8840\u3092\u56fa\u3081\u308b\u53cd\u5fdc\u304c\u59cb\u307e\u308a\u306b\u304f\u304f\u306a\u308a\u3001\u51fa\u8840\u304c\u6b62\u307e\u308a\u306b\u304f\u304f\u306a\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u75c7\u72b6<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>\u9f3b\u8840\u3001\u6b6f\u3050\u304d\u304b\u3089\u306e\u51fa\u8840\u3001\u3042\u3056\u304c\u3067\u304d\u3084\u3059\u3044<\/strong><\/li>\n\n\n\n<li><strong>\u6708\u7d4c\u904e\u591a<\/strong>\uff08\u5973\u6027\u3067\u306f\u6700\u521d\u306e\u75c7\u72b6\u306b\u306a\u308b\u3053\u3068\u304c\u591a\u3044\uff09<\/li>\n\n\n\n<li>\u629c\u6b6f\u3084\u624b\u8853\u306e\u3042\u3068\u306e\u6b62\u8840\u56f0\u96e3<\/li>\n\n\n\n<li><strong>\u91cd\u75c7\u4f8b\uff08\u6d3b\u60271%\u672a\u6e80\uff09<\/strong>\uff1a\u4e73\u5150\u671f\u306e\u982d\u84cb\u5185\u51fa\u8840\u3001\u95a2\u7bc0\u5185\u51fa\u8840<\/li>\n\n\n\n<li><strong>\u7121\u75c7\u72b6\u306e\u65b9\u3082\u3044\u307e\u3059<\/strong>\uff08\u8840\u6db2\u691c\u67fb\u3067PT\u3060\u3051\u304c\u5ef6\u9577\u3057\u3066\u3044\u308b\u3053\u3068\u304b\u3089\u898b\u3064\u304b\u308a\u307e\u3059\uff09<\/li>\n\n\n\n<li><strong>\u56e0\u5b50\u306e\u6d3b\u6027\u5024\u3068\u51fa\u8840\u306e\u91cd\u3055\u306f\u5fc5\u305a\u3057\u3082\u4e00\u81f4\u3057\u307e\u305b\u3093<\/strong><\/li>\n\n\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\">\u691c\u67fb\u30fb\u8a3a\u65ad<\/h2>\n\n\n\n<p>\u8840\u6db2\u691c\u67fb\u3067<strong>\u30d7\u30ed\u30c8\u30ed\u30f3\u30d3\u30f3\u6642\u9593\uff08PT\uff09\u3060\u3051\u304c\u5ef6\u9577\u3057\u3001APTT\u306f\u6b63\u5e38<\/strong>\u3068\u3044\u3046\u7279\u5fb4\u7684\u306a\u30d1\u30bf\u30fc\u30f3\u3092\u793a\u3057\u307e\u3059\u3002\u7b2cVII\u56e0\u5b50\u306e\u6d3b\u6027\u3092\u6e2c\u5b9a\u3057\u3066\u8a3a\u65ad\u3057\u3001<strong>F7<\/strong> \u907a\u4f1d\u5b50\u306e\u89e3\u6790\u306b\u3088\u3063\u3066\u78ba\u5b9a\u3057\u307e\u3059\u3002\u30d3\u30bf\u30df\u30f3K\u6b20\u4e4f\u3084\u809d\u969c\u5bb3\u3001\u6297\u51dd\u56fa\u85ac\u306e\u5f71\u97ff\u3068\u306e\u533a\u5225\u304c\u5fc5\u8981\u3067\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u6cbb\u7642<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>\u907a\u4f1d\u5b50\u7d44\u63db\u3048\u6d3b\u6027\u578b\u7b2cVII\u56e0\u5b50\u88fd\u5264\uff08rFVIIa\uff0f\u30ce\u30dc\u30bb\u30d6\u30f3\u00ae\uff09<\/strong>\uff1a\u51fa\u8840\u6642\u3084\u624b\u8853\u524d\u306b\u6295\u4e0e\u3057\u307e\u3059<\/li>\n\n\n\n<li>\u65b0\u9bae\u51cd\u7d50\u8840\u6f3f\u3001\u30d7\u30ed\u30c8\u30ed\u30f3\u30d3\u30f3\u8907\u5408\u4f53\u88fd\u5264<\/li>\n\n\n\n<li>\u91cd\u75c7\u4f8b\u3067\u306f<strong>\u5b9a\u671f\u7684\u306a\u88dc\u5145\u7642\u6cd5\uff08\u4e88\u9632\u6295\u4e0e\uff09<\/strong>\u3092\u884c\u3046\u3053\u3068\u304c\u3042\u308a\u307e\u3059<\/li>\n\n\n\n<li>\u6297\u7dda\u6eb6\u85ac\uff08\u30c8\u30e9\u30cd\u30ad\u30b5\u30e0\u9178\uff09\uff1a\u7c98\u819c\u304b\u3089\u306e\u51fa\u8840\u306b\u6709\u52b9\u3067\u3059<\/li>\n\n\n\n<li>\u6708\u7d4c\u904e\u591a\u306b\u306f\u30db\u30eb\u30e2\u30f3\u7642\u6cd5<\/li>\n\n\n\n<li><strong>\u30a2\u30b9\u30d4\u30ea\u30f3\u306a\u3069\u3001\u51fa\u8840\u3057\u3084\u3059\u304f\u306a\u308b\u85ac\u3092\u907f\u3051\u308b<\/strong><\/li>\n\n\n\n<li>\u629c\u6b6f\u3084\u624b\u8853\u306e\u524d\u306b\u306f\u3001\u5fc5\u305a\u8840\u6db2\u5185\u79d1\u306b\u3054\u76f8\u8ac7\u304f\u3060\u3055\u3044<\/li>\n\n\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\">\u3053\u306e\u75be\u60a3\u306f\u691c\u67fb\u3067\u308f\u304b\u308a\u307e\u3059<\/h2>\n\n\n\n<p>\u3053\u306e\u75be\u60a3\u306f\u3001\u539f\u56e0\u3068\u306a\u308b <strong>F7<\/strong> \u907a\u4f1d\u5b50\u3092\u8abf\u3079\u308b\u3053\u3068\u3067\u3001\u767a\u75c7\u524d\u3084\u51fa\u751f\u524d\u306b\u898b\u3064\u3051\u308b\u3053\u3068\u304c\u3067\u304d\u307e\u3059\u3002\u30d2\u30ed\u30af\u30ea\u30cb\u30c3\u30afNIPT\u3067\u306f\u6b21\u306e2\u3064\u306e\u691c\u67fb\u3092\u3054\u7528\u610f\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">\u30a8\u30af\u30bd\u30fc\u30e0\u89e3\u6790\u3092\u7528\u3044\u305f\u691c\u67fb\uff081,200\u7a2e\u985e\u4ee5\u4e0a\uff09<\/h3>\n\n\n\n<p>\u30a8\u30af\u30bd\u30fc\u30e0\u89e3\u6790\u306f\u3001\u907a\u4f1d\u5b50\u306e\u3046\u3061\u305f\u3093\u3071\u304f\u8cea\u306e\u8a2d\u8a08\u56f3\u306b\u3042\u305f\u308b\u90e8\u5206\uff08\u30a8\u30af\u30bd\u30f3\uff09\u3092\u307e\u3068\u3081\u3066\u8aad\u307f\u53d6\u308b\u691c\u67fb\u3067\u3059\u3002\u3053\u306e\u89e3\u6790\u3092\u884c\u3063\u305f\u3046\u3048\u3067\u3001<strong>F7<\/strong> \u907a\u4f1d\u5b50\u3092\u542b\u3080<strong>1,200\u7a2e\u985e\u4ee5\u4e0a<\/strong>\u306e\u907a\u4f1d\u5b50\u3092\u5bfe\u8c61\u306b\u8abf\u3079\u3001<strong>\u3053\u306e\u75be\u60a3\u306e\u539f\u56e0\u3068\u306a\u308b\u5909\u5316\u3092\u691c\u51fa\u3059\u308b\u3053\u3068\u304c\u53ef\u80fd\u3067\u3059<\/strong>\u3002\u56fd\u5185\u306e\u691c\u67fb\u6240\u3067\u884c\u3044\u3001\u7d50\u679c\u307e\u3067\u306e\u671f\u9593\u306f5\u9031\u9593\u301c7\u9031\u9593\u3067\u3059\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">\u30ad\u30e3\u30ea\u30a2\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u30c6\u30b9\u30c8\uff08228\u7a2e\u985e\uff09<\/h3>\n\n\n\n<p>\u5e38\u67d3\u8272\u4f53\u6f5c\u6027\uff08\u52a3\u6027\uff09\u907a\u4f1d\u306e\u75be\u60a3\u306f\u3001\u3054\u4e21\u89aa\u304c\u3069\u3061\u3089\u3082\u75c7\u72b6\u306e\u306a\u3044\u300c\u30ad\u30e3\u30ea\u30a2\uff08\u4fdd\u56e0\u8005\uff09\u300d\u3067\u3042\u308b\u3068\u304d\u306b\u3001<strong>4\u5206\u306e1\u306e\u78ba\u7387<\/strong>\u3067\u304a\u5b50\u3055\u307e\u304c\u767a\u75c7\u3057\u307e\u3059\u3002\u30ad\u30e3\u30ea\u30a2\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u30c6\u30b9\u30c8\u3067\u306f\u3001\u3054\u592b\u5a66\u304c\u3053\u306e\u75be\u60a3\u306e\u30ad\u30e3\u30ea\u30a2\u304b\u3069\u3046\u304b\u3092\u982c\u306e\u5185\u5074\u306e\u7c98\u819c\u304b\u3089\u8abf\u3079\u3001<strong>\u304a\u5b50\u3055\u307e\u306b\u53d7\u3051\u7d99\u304c\u308c\u308b\u53ef\u80fd\u6027\u3092\u3001\u598a\u5a20\u524d\u3084\u51fa\u751f\u524d\u306b\u4e88\u6e2c\u3059\u308b\u3053\u3068\u304c\u3067\u304d\u307e\u3059<\/strong>\u3002<\/p>\n\n\n\n<p>\u691c\u67fb\u306e\u5185\u5bb9\u30fb\u8cbb\u7528\u30fb\u7d50\u679c\u307e\u3067\u306e\u671f\u9593\u306f <a href=\"\/nipt\/nipt\/autosomal-recessive-inheritance\/\">\u30ad\u30e3\u30ea\u30a2\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u30c6\u30b9\u30c8228<\/a> \u306e\u30da\u30fc\u30b8\u3092\u3054\u89a7\u304f\u3060\u3055\u3044\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u5c02\u9580\u7684\u306a\u89e3\u8aac<\/h2>\n\n\n\n<p>\u7b2cVII\u56e0\u5b50\u6b20\u4e4f\u75c7\u306f <strong>F7<\/strong>\uff0813q34\uff09\u306e\u4e21\u30a2\u30ec\u30eb\u5909\u7570\u306b\u3088\u308b\u3001\u307e\u308c\u306a\u51dd\u56fa\u56e0\u5b50\u6b20\u4e4f\u75c7\u306e\u306a\u304b\u3067\u6700\u3082\u9ad8\u983b\u5ea6\uff081\/300,000\u301c500,000\uff09\u306e\u75be\u60a3\u3067\u3042\u308b\u3002FVII\u306f\u7d44\u7e54\u56e0\u5b50\uff08TF\uff09\u3068\u8907\u5408\u4f53\u3092\u5f62\u6210\u3057\u3001FX\u30fbFIX\u3092\u6d3b\u6027\u5316\u3057\u3066\u5916\u56e0\u7cfb\u51dd\u56fa\u3092\u958b\u59cb\u3059\u308b\u3002<\/p>\n\n\n\n<p><strong>PT\u5ef6\u9577\u30fbAPTT\u6b63\u5e38<\/strong>\u306e\u30d1\u30bf\u30fc\u30f3\u306f\u7b2cVII\u56e0\u5b50\u6b20\u4e4f\u306b\u7279\u5fb4\u7684\u3067\u3001\u4ed6\u306e\u51dd\u56fa\u56e0\u5b50\u6b20\u4e4f\u75c7\u3068\u306e\u9451\u5225\u306b\u6709\u7528\u3067\u3042\u308b\u3002\u30d3\u30bf\u30df\u30f3K\u4f9d\u5b58\u6027\u56e0\u5b50\u3067\u3042\u308b\u305f\u3081\u3001\u30d3\u30bf\u30df\u30f3K\u6b20\u4e4f\u30fb\u30ef\u30eb\u30d5\u30a1\u30ea\u30f3\u30fb\u809d\u969c\u5bb3\u306e\u9664\u5916\u3092\u8981\u3059\u308b\u3002<\/p>\n\n\n\n<p>\u672c\u75c7\u306e\u81e8\u5e8a\u7684\u7279\u5fb4\u306f<strong>\u51dd\u56fa\u6d3b\u6027\u3068\u51fa\u8840\u75c7\u72b6\u306e\u76f8\u95a2\u304c\u4e4f\u3057\u3044<\/strong>\u3053\u3068\u3067\u3042\u308b\u3002\u6d3b\u60271%\u672a\u6e80\u3067\u3082\u8efd\u5fae\u306a\u75c7\u72b6\u306b\u3068\u3069\u307e\u308b\u4f8b\u304c\u3042\u308b\u4e00\u65b9\u300110%\u7a0b\u5ea6\u3067\u3082\u91cd\u7be4\u306a\u51fa\u8840\u3092\u8d77\u3053\u3059\u4f8b\u304c\u3042\u308b\u3002\u3057\u305f\u304c\u3063\u3066\u6cbb\u7642\u65b9\u91dd\u306f\u6d3b\u6027\u5024\u306e\u307f\u3067\u306a\u304f\u51fa\u8840\u6b74\u306b\u57fa\u3065\u3044\u3066\u6c7a\u5b9a\u3059\u308b\u3002<\/p>\n\n\n\n<p>\u91cd\u75c7\u578b\u3067\u306f\u4e73\u5150\u671f\u306e\u982d\u84cb\u5185\u51fa\u8840\u304c\u4e88\u5f8c\u3092\u898f\u5b9a\u3057\u3001\u4e88\u9632\u7684\u88dc\u5145\u7642\u6cd5\u306e\u9069\u5fdc\u3068\u306a\u308b\u3002rFVIIa\u306f\u534a\u6e1b\u671f\u304c2\u301c4\u6642\u9593\u3068\u77ed\u3044\u305f\u3081\u3001\u5468\u8853\u671f\u306b\u306f\u983b\u56de\u6295\u4e0e\u3092\u8981\u3059\u308b\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u3088\u304f\u3042\u308b\u8cea\u554f<\/h2>\n\n\n\n<h3 class=\"wp-block-heading\">Q. \u8840\u6db2\u691c\u67fb\u3067\u7570\u5e38\u3092\u6307\u6458\u3055\u308c\u307e\u3057\u305f\u304c\u3001\u75c7\u72b6\u304c\u3042\u308a\u307e\u305b\u3093\u3002<\/h3>\n\n\n\n<p>A. \u3053\u306e\u75c5\u6c17\u3067\u306f\u3001\u7121\u75c7\u72b6\u306e\u307e\u307e\u898b\u3064\u304b\u308b\u65b9\u304c\u5c11\u306a\u304f\u3042\u308a\u307e\u305b\u3093\u3002\u305f\u3060\u3057\u624b\u8853\u3084\u629c\u6b6f\u306e\u524d\u306b\u306f\u5bfe\u5fdc\u304c\u5fc5\u8981\u3067\u3059\u306e\u3067\u3001\u5fc5\u305a\u4e3b\u6cbb\u533b\u306b\u304a\u4f1d\u3048\u304f\u3060\u3055\u3044\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">Q. \u56e0\u5b50\u306e\u5024\u304c\u4f4e\u3044\u3068\u5fc5\u305a\u91cd\u3044\u51fa\u8840\u304c\u8d77\u3053\u308a\u307e\u3059\u304b\uff1f<\/h3>\n\n\n\n<p>A. \u3044\u3044\u3048\u3002\u3053\u306e\u75c5\u6c17\u3067\u306f<strong>\u6570\u5024\u3068\u75c7\u72b6\u304c\u4e00\u81f4\u3057\u306a\u3044\u3053\u3068<\/strong>\u304c\u77e5\u3089\u308c\u3066\u3044\u307e\u3059\u3002\u3053\u308c\u307e\u3067\u306e\u51fa\u8840\u306e\u7d4c\u904e\u3092\u3082\u3068\u306b\u6cbb\u7642\u65b9\u91dd\u3092\u6c7a\u3081\u307e\u3059\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">Q. \u629c\u6b6f\u3092\u53d7\u3051\u308b\u3053\u3068\u306b\u306a\u308a\u307e\u3057\u305f\u3002<\/h3>\n\n\n\n<p>A. \u4e8b\u524d\u306b\u8840\u6db2\u5185\u79d1\u306b\u3054\u76f8\u8ac7\u304f\u3060\u3055\u3044\u3002\u88fd\u5264\u306e\u6295\u4e0e\u3084\u30c8\u30e9\u30cd\u30ad\u30b5\u30e0\u9178\u306e\u4f7f\u7528\u3067\u3001\u5b89\u5168\u306b\u53d7\u3051\u3089\u308c\u307e\u3059\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">Q. \u6708\u7d4c\u91cf\u304c\u591a\u3044\u306e\u3067\u3059\u304c\u95a2\u4fc2\u3042\u308a\u307e\u3059\u304b\uff1f<\/h3>\n\n\n\n<p>A. \u5973\u6027\u3067\u306f\u3053\u308c\u304c\u6700\u521d\u306e\u75c7\u72b6\u306b\u306a\u308b\u3053\u3068\u304c\u591a\u304f\u3042\u308a\u307e\u3059\u3002\u30db\u30eb\u30e2\u30f3\u7642\u6cd5\u3084\u6297\u7dda\u6eb6\u85ac\u3067\u5bfe\u5fdc\u3067\u304d\u307e\u3059\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">Q. \u907f\u3051\u305f\u307b\u3046\u304c\u3088\u3044\u85ac\u306f\u3042\u308a\u307e\u3059\u304b\uff1f<\/h3>\n\n\n\n<p>A. \u30a2\u30b9\u30d4\u30ea\u30f3\u3084\u4e00\u90e8\u306e\u89e3\u71b1\u93ae\u75db\u85ac\u306a\u3069\u3001\u51fa\u8840\u3057\u3084\u3059\u304f\u306a\u308b\u85ac\u306f\u907f\u3051\u3066\u304f\u3060\u3055\u3044\u3002\u5e02\u8ca9\u85ac\u3092\u4f7f\u3046\u524d\u306b\u3054\u76f8\u8ac7\u304f\u3060\u3055\u3044\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u53c2\u8003\u6587\u732e<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Mariani G, Bernardi F. Factor VII Deficiency. <em>Semin Thromb Hemost<\/em>. 2009;35(4):400-406.<\/li>\n\n\n\n<li>Napolitano M, Giansily-Blaizot M, Dolce A, et al. Prophylaxis in congenital factor VII deficiency: indications, efficacy and safety. Results from the Seven Treatment Evaluation Registry (STER). <em>Haematologica<\/em>. 2013;98(4):538-544.<\/li>\n\n\n\n<li>Mariani G, Herrmann FH, Dolce A, et al. Clinical phenotypes and factor VII genotype in congenital factor VII deficiency. <em>Thromb Haemost<\/em>. 2005;93(3):481-487.<\/li>\n\n\n\n<li>OMIM #227500 Factor VII deficiency<\/li>\n\n\n<\/ul>\n","protected":false},"featured_media":0,"menu_order":0,"template":"page_gd.php","class_list":["post-136687","genetic-diseases","type-genetic-diseases","status-publish","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases\/136687","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases"}],"about":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/types\/genetic-diseases"}],"version-history":[{"count":1,"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases\/136687\/revisions"}],"predecessor-version":[{"id":137057,"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases\/136687\/revisions\/137057"}],"wp:attachment":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/media?parent=136687"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}