{"id":33648,"date":"2022-07-11T17:28:52","date_gmt":"2022-07-11T08:28:52","guid":{"rendered":"https:\/\/www.hiro-clinic.or.jp\/nipt\/?page_id=33648"},"modified":"2026-04-28T13:17:47","modified_gmt":"2026-04-28T04:17:47","slug":"primary-hyperoxaluria-type-3%e3%80%80","status":"publish","type":"genetic-diseases","link":"https:\/\/www.hiro-clinic.or.jp\/nipt\/genetic-diseases2\/primary-hyperoxaluria-type-3%e3%80%80\/","title":{"rendered":"\u539f\u767a\u6027\u9ad8\u30b7\u30e5\u30a6\u9178\u5c3f\u75c73\u578b\u3000"},"content":{"rendered":"\n<h2 class=\"wp-block-heading\">\u6982\u8981<\/h2>\n\n\n\n<p>\u539f\u767a\u6027\u9ad8\u30b7\u30e5\u30a6\u9178\u5c3f\u75c73\u578b\uff08PH3\uff09\u306f\u3001\u5c0f\u5150\u671f\u307e\u305f\u306f\u9752\u5e74\u671f\u306b\u59cb\u307e\u308b\u30b7\u30e5\u30a6\u9178\u30ab\u30eb\u30b7\u30a6\u30e0\u7d50\u77f3\u306e\u518d\u767a\u3068\u3001\u814e\u77f3\u7070\u5316\u75c7\u307e\u305f\u306f\u814e\u6a5f\u80fd\u306e\u4f4e\u4e0b\u3092\u7279\u5fb4\u3068\u3057\u307e\u3059\u3002<\/p>\n\n\n\n<p>PH3\u7d50\u77f3\u5f62\u6210\u306e\u3042\u308b\u4eba\u306e50\uff05-65\uff05\u306f\u30015\u6b73\u3088\u308a\u524d\u306b\u767a\u75c7\u3057\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u77f3\u306e\u6d3b\u52d5\u306e\u983b\u5ea6\u3068\u91cd\u75c7\u5ea6\u306f\u3001\u9752\u5e74\u671f\u3068\u6210\u4eba\u671f\u306b\u3088\u3063\u3066\u843d\u3061\u7740\u304f\u3088\u3046\u306b\u898b\u3048\u308b\u3053\u3068\u304c\u3088\u304f\u3042\u308a\u307e\u3059\u304c\u3001\u77f3\u306e\u5f62\u6210\u306f\u751f\u6daf\u3092\u901a\u3058\u3066\u767a\u751f\u3059\u308b\u53ef\u80fd\u6027\u304c\u3042\u308a\u3001\u4e00\u90e8\u306e\u6210\u4eba\u306f\u591a\u304f\u306e\u77f3\u3092\u6301\u3063\u3066\u3044\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u73fe\u5728\u307e\u3067\u3001\u5168\u8eab\u6027\u30aa\u30ad\u30b5\u30ed\u30b7\u30b9\u306fPH3\u3067\u5831\u544a\u3055\u308c\u3066\u3044\u307e\u305b\u3093\u3002<\/p>\n\n\n\n<p>\u4ed6\u306e\u81d3\u5668\u306b\u5f71\u97ff\u3092\u4e0e\u3048\u308b\u53ef\u80fd\u6027\u306e\u3042\u308bPH1\u3084PH2\u3068\u306f\u7570\u306a\u308a\u3001PH3\u3067\u306e\u30b7\u30e5\u30a6\u9178\u5869\u306e\u84c4\u7a4d\u306f\u814e\u81d3\u306e\u307f\u3068\u306a\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u75ab\u5b66<\/h2>\n\n\n\n<p>PH\u75c7\u4f8b\u306e\u7d0410\uff05\u306fPH3\u3068\u306a\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u4eba\u53e3\u306b\u304a\u3051\u308bPH3\u306e\u767a\u751f\u7387\u306f165,000\u4eba\u306e\u51fa\u751f\u306b1\u4eba\u3067\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u539f\u56e0<\/h2>\n\n\n\n<p>PH3\u306f\u6f5c\u6027\u907a\u4f1d\u75be\u60a3\u3067\u3059\u3002HOGA1\u907a\u4f1d\u5b50\u306e\u6709\u5bb3\u306a\u907a\u4f1d\u7684\u5909\u5316\uff08\u7a81\u7136\u5909\u7570\uff09\u306b\u3088\u3063\u3066\u5f15\u304d\u8d77\u3053\u3055\u308c\u307e\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u75c7\u72b6<\/h2>\n\n\n\n<p>\u814e\u81d3\u7d50\u77f3\u3092\u767a\u75c7\u3059\u308b\u30ea\u30b9\u30af\u304c\u9ad8\u304f\u306a\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u75c7\u72b6\u306f\u4e73\u5150\u671f\u304b\u3089\u6210\u4eba\u671f\u307e\u3067\u3044\u3064\u3067\u3082\u767a\u75c7\u3059\u308b\u53ef\u80fd\u6027\u304c\u3042\u308a\u307e\u3059\u3002\u7f79\u60a3\u3057\u305f\u5834\u5408\u7d0450\uff05\u304c5\u6b73\u307e\u3067\u306b\u814e\u7d50\u77f3\u3092\u767a\u75c7\u3057\u307e\u3059\u304c\u3001\u591a\u304f\u306e\u4eba\u306f\u6210\u4eba\u671f\u307e\u3067\u306b\u814e\u81d3\u7d50\u77f3\u306e\u767a\u751f\u7387\u304c\u4f4e\u4e0b\u3057\u307e\u3059\u3002\u6210\u4eba\u306b\u306a\u308b\u307e\u3067\u75c7\u72b6\u304c\u51fa\u306a\u3044\u4eba\u3082\u3044\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u983b\u7e41\u306a\u814e\u7d50\u77f3\u306f\u814e\u81d3\u6a5f\u80fd\u306b\u5f71\u97ff\u3092\u4e0e\u3048\u308b\u53ef\u80fd\u6027\u304c\u3042\u308a\u307e\u3059\u304c\u3001\u305f\u3060\u3057\u3001PH3\u306e\u60a3\u8005\u304c\u814e\u4e0d\u5168\u306b\u9032\u884c\u3059\u308b\u3053\u3068\u306f\u3081\u3063\u305f\u306b\u3042\u308a\u307e\u305b\u3093\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u8a3a\u65ad<\/h2>\n\n\n\n<p>\u4ee5\u4e0b\u306e\u6240\u898b\u304b\u3089\u8a3a\u65ad\u3057\u307e\u3059\u3002<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>\u30b7\u30e5\u30a6\u9178\u30ab\u30eb\u30b7\u30a6\u30e0\u814e\u7d50\u77f3\u307e\u305f\u306f\u814e\u77f3\u7070\u5316\u75c7<\/li>\n\n\n\n<li>\u30b7\u30e5\u30a6\u9178\u5c3f&gt; 0.7 mmol \/ 1.73 m 2\/24\u6642\u9593\uff08\u814e\u6a5f\u80fd\u304c\u7dad\u6301\u3055\u308c\u3066\u3044\u308b\u60a3\u8005\uff09<\/li>\n\n\n\n<li>\u8840\u6f3f\u30b7\u30e5\u30a6\u9178\u5869\u6fc3\u5ea6\u306e\u4e0a\u6607\uff08\u7279\u306b\u814e\u6a5f\u80fd\u304c\u4f4e\u4e0b\u3057\u3066\u3044\u308b\u60a3\u8005\uff09<\/li>\n\n\n\n<li>HOGA1\u306e\u4e8c\u5bfe\u7acb\u907a\u4f1d\u5b50\uff08\u30db\u30e2\u63a5\u5408\u307e\u305f\u306f\u8907\u5408\u30d8\u30c6\u30ed\u63a5\u5408\uff09\u75c5\u539f\u6027\u591a\u69d8\u4f53<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\">\u6cbb\u7642<\/h2>\n\n\n\n<p>\u4e3b\u306b\u30b7\u30e5\u30a6\u9178\u30ab\u30eb\u30b7\u30a6\u30e0\u306e\u5f62\u6210\u3068\u6c88\u7740\u3092\u9632\u3050\u3053\u3068\u3092\u76ee\u7684\u3068\u3057\u3066\u3044\u307e\u3059\u3002\u30b7\u30e5\u30a6\u9178\u5869\u30ec\u30d9\u30eb\u3092\u4e0b\u3052\u3001\u814e\u81d3\u7d50\u77f3\u306e\u5f62\u6210\u3092\u6291\u5236\u3059\u308b\u306e\u306b\u5f79\u7acb\u3064\u85ac\u3084\u30d3\u30bf\u30df\u30f3\u3092\u5185\u670d\u3059\u308b\u3053\u3068\u304c\u3042\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u30b7\u30e5\u30a6\u9178\u5869\u3092\u591a\u304f\u542b\u3080\u98df\u54c1\u306e\u98df\u4e8b\u5236\u9650\u3092\u884c\u3046\u3053\u3068\u3082\u3042\u308a\u307e\u3059\u3002<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">\u4e88\u5f8c<\/h2>\n\n\n\n<p>\u60a3\u8005\u306e\u591a\u304f\u306f\u3001\u6210\u4eba\u671f\u306b\u9054\u3059\u308b\u3068\u814e\u81d3\u7d50\u77f3\u306e\u5f62\u6210\u304c\u6e1b\u5c11\u3057\u307e\u3059\u3002<\/p>\n\n\n\n<p>\u307b\u3068\u3093\u3069\u306e\u4eba\u306e\u5834\u5408\u3067\u814e\u81d3\u306e\u79fb\u690d\u306f\u5fc5\u8981\u306a\u304f\u3001\u814e\u4e0d\u5168\u3078\u306e\u9032\u884c\u306e\u5831\u544a\u306f\u307b\u3068\u3093\u3069\u3042\u308a\u307e\u305b\u3093\u3002<\/p>\n\n\n\n<div class=\"wp-block-group references\"><div class=\"wp-block-group__inner-container is-layout-flow wp-block-group-is-layout-flow\">\n<p>\u3010\u53c2\u8003\u6587\u732e\u3011<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>NIH &#8211;<a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK316514\/\" data-type=\"URL\" data-id=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK316514\/\">Primary Hyperoxaluria Type 3<\/a><\/li>\n\n\n\n<li>Myriad genetics &#8211; <a href=\"https:\/\/myriad.com\/womens-health\/diseases\/primary-hyperoxaluria-type-3\/\" data-type=\"URL\" data-id=\"https:\/\/myriad.com\/womens-health\/diseases\/primary-hyperoxaluria-type-3\/\">Primary Hyperoxaluria Type 3<\/a><\/li>\n<\/ul>\n<\/div><\/div>\n","protected":false},"featured_media":0,"menu_order":32,"template":"page_gd.php","class_list":["post-33648","genetic-diseases","type-genetic-diseases","status-publish","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases\/33648","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases"}],"about":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/types\/genetic-diseases"}],"version-history":[{"count":6,"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases\/33648\/revisions"}],"predecessor-version":[{"id":127728,"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/genetic-diseases\/33648\/revisions\/127728"}],"wp:attachment":[{"href":"https:\/\/www.hiro-clinic.or.jp\/nipt\/wp-json\/wp\/v2\/media?parent=33648"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}